Chinhu Chidiki Chinozivikanwa Chikonzero Chokunzwa Kurasikirwa
Mondini syndrome, inozivikanwawo seM Mondini dysplasia kana kuti Mondini inorondedzera, inotsanangura mamiriro ezvinhu apo cochlea haina kukwana, iine kutendeuka imwe chete nehafu pane nzvimbo inowanzoita maviri nehafu kutendeuka. Mamiriro acho akatanga kurondedzerwa muna 1791 nachiremba Carlo Mondini mune imwe nyaya yakanzi "The Anatomic Section of a Boy Born Injured." Shanduro yakabva kune yekutanga yechiLatini yechinyorwa yakabudiswa muna 1997.
Nyaya yepakutanga yaCarlo Mondini yakanga ine tsanangudzo yakajeka yezvinyorwa zvinotumidzwa zita rake. Kwemakore, vamwe vanachiremba vakashandisa shoko iri kutsanangura rimwe bony cochlear kusagadzikana. Paunokurukura nezveMondini kusagadzikana, zvakakosha kuva netsanangudzo yakajeka yekichlea nedzimwe nhengo dzekunze dzekunze sezvo zita rokuti 'Mondini' rinogona kuvhiringidza.
Zvinokonzera
Iyi isangano (ikozvino pakuberekwa) chinokonzera kurasikirwa kwekunzwa. Nhoroondo ye Mondini inowanikwa apo kune kupesana mukuvandudzwa kwenzeve yomukati panguva yevhiki yechinomwe yekugumira. Izvi zvinogona kukanganisa imwe kana nzeve mbiri uye inogona kurega kana kuitika nedzimwe nhepfenyuro dzekunzwa kana syndromes. Syndromes iyo inozivikanwa kuti inobatanidza naMondini kusagadzikana inosanganisira Pendred Syndrome, DiGeorge Syndrome, Klippel Feil Syndrome, Fountain Syndrome, Wildervanck Syndrome, CHARGE syndrome, uye dzimwe chromosomal trisomies.
Kune zviitiko apo Mondini kusagadzikana kwave kwakabatanidzwa kune autosomal inowanikwa uye inotenderera yakawanda nhaka yemaitiro pamwe chete nekuve yakangoitika.
Kuziva
Kuongororwa kweMondini kusagadzikana kunowanikwa nekuongorora kwemashoko, zvakadai sekugadziriswa kweT CT maitiro emapfupa epanguva.
Kunzwa kurasikirwa uye kurapwa
Kurasikirwa kwekunzwa kunobatanidza naMondini kusagadzikana kunogona kusiyana, kunyange zvazvo kazhinji kunowedzera. Kunzwa rubatsiro kunokurudzirwa kana pane zvakakwana zvekunzwa kunzwa kuti zvibatsire. Mumamiriro ezvinhu apo manzwiro ekunzwa haabatsiri, cochlear implantation yaitwa kubudirire.
Zvimwe Zvokufungisisa
Vanhu vane Mondini kusagadzikana kunogona kunge vari pangozi yakakura ye meningitis. Izvo zvinokonzera kukanganisa zvinogona kugadzira nzvimbo inonyoresa yokupinda kumvura inenge yakakomberedzwa neuropi uye musipinha. Mumamiriro ezvinhu apo pane zviitiko zve (meningitis) zvakawanda (kana zvekare) zvekare, chirwere chokuvhara ichi chinopindira chinogona kuratidzwa.
Kunyora kweMondini kunogonawo kukanganisa kushandiswa kwehutano hwekunze kwenzeve. Vana vane maMformini malformations vanogona kuratidza kunonoka kwekuvandudzwa mumotokari yavo yekufambisa nekuda kwekuderedza kuwedzerwa kuuropi kubva muhutano hwavo. Mune dzimwe nguva, nyaya dzekuenzanisa hazviitike kusvikira munhu mukuru.
> Sources:
> Hain, T (2012). Mondini naMichel Maitiro emunzeve yomukati. Chizutu uye Kuenzanisa.
> Lo, W (1999). Chii chinonzi 'Mondini' uye Zita Rakaita Sei? American Journal of Neuroradiology.
> Mondini C. Minor mabasa aCarlo> Mondini: > The anatomic chikamu chemukomana akaberekwa ari matsi. Am J Otol 1997; 18: 288-293
> Mondini Dysplasia (2012). Hofisi yeRare Disease Research.