Maererano neKawasaki Disease

Mhando yeArthritis uye Form of Systemic Vasculitis

Kawasaki chirwere nderimwe remapoka anopfuura 100 arthritis, maererano neArthritis Foundation. Kawasaki chirwere chimiro che systemic vasculitis chinokura muvana vaduku; 80% yevarwere veKawasaki vari pasi pemakore mashanu.

Tomasaku Kawasaki akatanga kuziva chirwere ichi muna 1967 muJapan. Asati asarudzwa sechirwere cheKawasaki, chiitiko chacho chaizivikanwa sechirwere chemuviri chechirmodoma.

Inonziwo chirwere cheKawasaki, Kawasaki's syndrome uye infantile polyarteritis.

Zviratidzo

Kawasaki chirwere chinogona kuenzaniswa nekugadzirwa kwe coronary arteritis (inflammation of the coronary arteries) uye kuumbwa kweanaurysms. MuUnited States, chirwere cheKawasaki chinoonekwa sechikonzero chinotungamirira chechirwere chemwoyo muvana.

Kawasaki chirwere chinokura nokukurumidza uye chinotyisa chirwere chinotyisa pane imwe nguva yevhiki. Kazhinji, chiitiko chacho chinogadzirisa. Kunyangwe zvazvo ichigadzirisa, zvakadaro, kunogona kuva nematambudziko emwoyo makore akazotevera.

Zvimwe zviratidzo zvine chokuita nehosha yeKawasaki zvinosanganisira:

Zvimwe zviitiko zvisingawanzoitiki zvinogona kuitika nehosha yeKawasaki zvinosanganisira aseptic meningitis, yakaipa pyuria uye urethritis, chirwere, kurwadziwa mumimba, pericardial effusion , obstructive jaundice, uye hydrops ye gallbladder.

Cause

Vamwe vanofungidzira kuti kune chirwere chinotapukira chechipatara cheKawasaki, asi hapana chakaonekwa. Kune huwandu hwezvisizvo zvehutachiona hunobatanidzwa nechirwere cheKawasaki, uye vamwe vanotenda kuti iyo ndiyo mamiriro ekudzivirira .

Kuwanda

MuUnited States, chirwere cheKawasaki chinokanganisa vana 4 000 gore negore. Iyo yakawanda zvikuru muJapan apo yakawanikwa ne5000 kusvika ku6 000 matambudziko gore negore.

Mishonga

Kamwe chirwere ichi chikaonekwa, chirwere chinokurumidza chinokurudzirwa kuitira kuti kukanganisa kwemaketari emakemikari nemwoyo zvinogona kudziviswa. Intravenous immune globulin (IVIG) inopiwa muhotera yakanyanya inofungidzirwa kuti inorapwa yeKawasaki chirwere. High-dose aspirin inowanzova chikamu cherongwa hwekurapa pamwe chete. Glucocorticoids haigoni kushandiswa kurapa chirwere cheKawasaki.

Nokurapa kwokutanga kwechirwere cheKawasaki, kuzorora kwakakwana kunogona kuitika kune vakawanda, asi 2 muzana yevarwere veKaasaki varwere vanofa nematambudziko e coronary artery inflammation. Zvinokurudzirwa kuti varwere vane chirwere cheKawasaki vane EKG (echocardiogram) imwe neimwe kana makore maviri kuti vaongorore zvinetso zvemoyo.

Sources:

Vasculitides. Kawasaki's Disease (Chitsauko 21). Primer paRheumatic Diseases . 13 Edition. Yakabudiswa neArthritis Foundation. Klippel J. et al.

Haisi Kungoerekana Kuwedzera Marwadzo . Kawasaki Disease Chapter 17. Thomas JA Lehman, MD. Oxford University Press. 2004.

Kawasaki Disease. MedlinePlus. NLM uye NIH. 11/29/2006.