Kuongorora Guillain-Barré Syndrome

Zvaunotarisira Paunenge Uchiongorora

Guillain-Barré chirwere chisingawanzoitiki umo muviri wemuviri wake unokanganisa zvikamu zvehutachiona hwehutachiona hwehutachiona uye hunotuma varwi vanorwisa zvirwere izvozvo. Chigumisiro chinowanzoitika ndechekusava nesimba uye kushaya simba kunotanga pane zvigunwe zveminwe nezvigunwe uye zvinopararira mukati kumunhu.

Inenge makumi matatu kubva muzana yenguva, utera uhwu hunova hwakanyanya zvokuti murwere haagoni kuzvifema pachavo.

Ivowo havagoni kumedza kudya kana salivha kunze kwekunge "zvichidzika pasi zvisina kunaka" uye mumapapu avo. Nokuda kwezvikonzero izvi, Guillain-Barré anogona kuisa upenyu hwake pangozi uye anoda kutarisirwa pedyo nevashandi vezvokurapa, kazhinji vari muchipatara. Pano uchaona kuti vanachiremba vanoona sei kana murwere ane Guillain-Barré syndrome.

Kuongorora Panyama

Kunze kwekutora nhoroondo yakanyatsogadzirisa kusarudza kana Guillain-Barré angangodaro, chiremba achatsvaga zvimwe zviwanikwa pakuongorora mumuviri. Nemhaka yokuti mishonga inoputika inowanikwa muGuillain-Barré, mafungiro , akadai sewaini-jerk reflex, kazhinji haasipo. Chiremba achaongororawo maoko nemakumbo kuti aone kana vasina simba uye vanoedza kuongorora kana kuona kuti kune chero rudzi rwekushaya simba. Vanachiremba vane hanya naGuillain-Barré vachanyatsocherechedza mitsipa yepamusoro nokuti kana izvi zvakuvadzwa, zvinogona kutungamirira kudiwa kwekudzivirira kana kushandiswa kwemajini kuitira kuti murwere arambe achifema.

Electromyography uye Nerve Conduction Studies (EMG / NCS)

Apo chirwere chendaneti chinotambudzwa nechirwere, chinoshandura mararamiro emagetsi emagetsi akatumirwa uye akagamuchirwa mumutambo iwoyo. Nokuyera kuchinja uku nemishonga inokosha, vanachiremba vanogona kutaurira chete kana chimwe chinhu chakashata, asiwo izvo zvikamu zvehutano zvinosangana zvakanyanya.

Iyi ruzivo inogona kubatsira kutungamira zvisarudzo pamusoro pezvokurapa, pamwe nekupa chiremba pfungwa yekuti chirwere chacho chakanyanya sei uye kuti zvichazotora nguva yakareba sei kuti munhu awanezve.

Somuenzaniso, kana mumwe munhu ane utera hunopararira kumusoro saGuillain-Barré anogona, zvidzidzo izvi zvekugadzira magetsi zvinogona kubatsira kuziva kana axon kana kuti myelin sheath yeropa iri kurwiswa. Myelin anopoteredza axon uye anobatsira zviratidzo zvemagetsi zvinokurumidza kukunda kupfuura zvavangaita. Kana magetsi achiyerera zvishoma nezvishoma kuburikidza nenyasha, vanachiremba vangave vachifungidzira kuti myelin iri kurwiswa, pane izvo zviitiko chimiro chakajairika chaGuillain-Barré ndicho chikonzero chinokonzera.

Kune rumwe rutivi, kana axon ichirwiswa, chiratidzo chiduku chegetsi chichachiita. Kana izvi zvichienzaniswa nedzidzo dzekunyatsodzidza, imwe yezvinyorwa zvisingawanzoshandiswa zveGuillain-Barré zvingave zvine mhosva. Kana izvi zvichikanganisa zvose zvinonzwika uye motori neuron, murwere anogona kunge ane motokari yakaoma uye inokonzerwa neuropathy neuropathy (AMSAN), zvakasiyana-siyana zvinoshungurudza zvinoda kurapa kwakasimba uye kurapa kwakakura kwekugadzirisa.

Lumbar Puncture

Muchivhiringidziro chemagetsi chinokonzera hurongwa hwemitsipa, chiyero chemapuroteni mumutumbi we cerebrospinal fluid (CSF) inogona kuva yakakwirira.

Nokuda kwechikonzero ichi, kuvharwa kwechimbwa kunogona kuitwa. Kuita kuputika kwekambani kunogona kubatsirawo kutonga kunze kwevamwe vanogona kufanana naGuillain-Barré, zvakadai sezvirwere.

Dambudziko reRopa

Hazvishamisi kuti vanachiremba varonge kuongorora ropa kuti vabatsire kuongorora Guillain-Barré syndrome. Mune zvimwe zviitiko, izvi zvinogona kubatsira kuwana an antibody ane mutoro. Somuenzaniso, kusiyana kweMiller-Fisher kwaGuillain-Barré kunowanzobatanidzwa neAnticoric anonzi GQ1b. Kuwana uyu antibody kunotsigira kuongororwa kweMiller-Fisher kushandiswa, uye kunogona kuita kuti chiremba ave akangwarira pamusoro pezvinodiwa mune ramangwana rekudzidzira.

Kuyera ropa kunobatsirawo pakutonga kunze kwemamwe mamiriro ezvinhu anogona kuonekwa akafanana naGuillain-Barré syndrome.

Zvichienderana nezvakaitika uye kuongorora muviri, chiremba anogona kuedza zviratidzo zvekenza , utachiona, kana kuti chepfu, dzakadai se mercury.

Zvakakosha kuziva chaicho chinokonzera dambudziko kuitira kuti usarega kupa mishonga isina kunaka. Kushandisa kuonekwa kwaGuillain-Barre kunobvumira vashandi vezvokurapa kuti vafunge nezvekurapa kwakanaka, uye vanogona kukupa mamwe mashoko pamusoro pezvinofanira kutarisira apo chirwere chinopfuurira, kuti iwe uchakurumidze kudzoka sei, uye rudzi rwekubatsira kwaunoda kuti udzoke pane wako tsoka zvakare.

Sources:

Ropper AH, Samuels MA. Adams naVictor's Principles of Neurology, 9th ed: The McGraw-Hill Companies, Inc., 2009. McCabe MP, O'Connor EJ.

Yuen T. Saka, Continuum: Peripheral Neuropathies, Immune-Mediated Neuropathies, Bhuku 18, Nhamba 1, February 2012.