Chimwe chinhu icho vanhu vane lymphoma nedzimwe mhando dzekenza yeropa vanowanzobata nadzo, ingave sechikamu chechirwere chavo kana sechikamu chechirwere chekurapa, kunoderedza kushanda kwekudzivirirwa mumuviri uye kukanganisa kutapukirwa. Dzimwe nguva vanhu vane kenza yeropa vane maitiro asina kukodzera ekirasi rimwe remasvomhu asi vamwe vane boka rinopfuura rimwechete vakavhiringidzika (IgA uye IgG mapoka maviri emasikirwo akaitwa nemajekiseni mamwe emasero eropa emuviri ; IgM isirasi yechitatu).
Ndeipi migumisiro yezvizvi zvisingaenzaniswi, uye vanogona kurapwa sei?
Zvirwere zvinogona kuguma kubva kuAnormal Antibody Levels
Zvirwere zvinowanzoitika, kunyanya kuputika kwezvirwere, zvirwere zvinowanzoonekwa kune varwere vane Waldenström's , rudzi rwusingaiti Hodgkin lymphoma , uye rungangodaro rwakabatana nekuvapo kwemazinga ehurwere-asi kunobva pane.
Nekuremekedza vanhu vasina kusimba muIgA (iyo inobatanidzwa munharaunda yemuviri inenge iri mumakumbo emumakumbo, zvakadai seyendarira yemhepo), chibatanidzwa kune hutachiwana hwehuwandu hunoita sechisina simba. Kutaura zvazviri, vanhu vanoberekwa vane kukwana mukirasi iyi ye anti-antibody chete havawanzo zviratidzo.
Vanachiremba vanowanzoramba vachiedza maitiro e- antibody . Somuenzaniso, akapona muWaldenström, Jennifer Killam, uyo akanga asiya Air Force Major, akataura kuti mumamiriro ake ose maitiro ake evanhu vese anowanzogadzikana kubuda. "Vanachiremba vangu vanoda kuchengetedza chengeteredze nguva dzose pamazinga angu anorusikisi-IgA, IgG, uye IgM.
MaMigM angu aya ari pasi pekutonga, asi ini handiri mukuregererwa, "akadaro Killam.
Mune Major Killam's kind of lymphoma, uye mamwe marudzi akasiyana-siyana emararamiro eropa ,wo masero anorwara anounza zvakanyanya kuwanda kwemaproteni anopinda muropa; mukati maro, inenge yakawandisa yakawanda yeAgM antibodies.
Chimwe chekurapa kwake kuedza kuunza mazinga aya kusvika kune chaiwo. Kunyange zvazvo chirongwa chake cheGG chave chiri pasi uye mumutambo wakanaka, maitiro ake egg antibody anowedzerawo-akadzika-uye IgG chinhu chikuru chinorwarisa-kupikisa anorifuta.
Kazhinji IgG mazinga ari pamusoro pe 800 mg / dL. Matsi makuru eKillam kusvika ku 200 mg / dL, izvo zvinoita kuti ave akakonzerwa nehosha. Saka, masvondo matanhatu ese anoenda kuGuta reTariro Medical Centre kwemaawa mana kusvika kumatanhatu kuti awane maGG levels zvakare. Anogamuchirwa muchero unozivikanwa seVIG.
IVIG Therapy
IVIG ndiyo chaiyo chirwere chakange chave chiripo kwemakumi emakore uye chinoshandiswa kurapa varwere vane marudzi akawanda ezvirwere. I IV inomirira kuvhara uye IG inomiririra immunoglobulin (izwi rezvesayenzi remapurogiramu anonzi antibody).
IVIG yakatanga kuratidzwa kuti inoshanda mune chirwere chinonzi autoimmune idiopathic thrombocytopenic purpura (ITP) muna 1981. Kubvira ipapo, rwendo rurefu rwezvirwere zvinoratidzika kuti runopindura zvakanaka kune IVIG rave richikura. Rimwe remashandisirwo makuru eVIG nderokudzorera maitiro evanhu vanoripikisa, asi iyo iri kure nekushandiswa chete.
IVIGs mishonga inogona kusungirirwa muhomwe yekushandiswa kwemvura mukati memawere. Izvo zvinokonzerwa nePlasma yevanhu yakasanganiswa, zvinoreva kuti mabhegi aya ane maGG antibodies kubva kuvanhu vakasiyana-siyana, vakasiyana-siyana vanopa utano hwakanaka, uye zvigadzirwa zvinowanzo zvine zvinopfuura 95 muzana unmodified IgG, uye zvinongorondedzera zviyero zve immunoglobulin A (IgA) kana immunoglobulin M ( IgM).
Kuunganidzwa kwezvirwere zvinopindura ku IVIG kunoshamisa uye urongwa hunogona kuratidza kukosha kwehutano hwehutano hwakanaka mumarudzi ose ezvirwere zvakasiyana.
Zvishandiso zveVIV Therapy
Heino shanduro yekushandiswa kweVIV.
Immunodeficiency: Izvi zvinosanganisira mitemo iyo vanhu vanoberekwa nayo asiwo zvirwere zvinotora zvirwere pamuviri wezvirwere semuviri saiyo chronic lymphocytic leukemia (CLL) uye akawanda myeloma. Zvimwewo zvinosanganisira zvirwere zvekudzivirira muviri zvinowedzera maererano neurongwa apo kurapwa kunodzvinyirira kushandiswa kweanorifomu mumuviri.
Zvirwere: Mune zvimwe zviitiko, kune mamiriro ezvinhu umo munhu ane nguva yakawanda kana kuti anokonzera zvirwere anogona kubatsirwa kubva ku IVIG.
Zvimwe zvirwere zvehutachiona, zvakadai sehutachiona husingaperi hwepatrovovirus hwakaoma neanemia, inosanganiswa mune izvi.
Zvirongwa zvekudzivirira muviri / Inflammatory: Kuwedzera pakugadzirisa idiopathic thrombocytopenic purpura, iyo iyo IVIG yakatanga kuratidzwa inoshanda muna 1981, zvimwe zvinhu zvakadai saGuillain-Barré syndrome, zvirwere zveKaasaki, uye zvirwere zvinokonzerwa neHIV zvinosanganiswa mune izvi.
Zvimwe Mamiriro: Dzimwe zvirwere zvinosanganisira nerve, dzinonzi chronic neuropathies, dzinogona kuchinjwa neVIG. Kugadziriswa kwekutsvaga kwepasi uye kushandiswa kwechirwere chemuviri chinopesana nehutachiona hunowirawo munharaunda iyi.
Kurarama NaWalddenström's, Kuita NeZvani-Maitiro
Major Killam vakataura kuti, panguva ino, chirwere chake chakasimba. Zvirwere zvaro zvakamuunza iye IgM mazinga pasi kuitira kuti asafanirwa kunetseka zvakanyanya pamusoro pezvimwe zvezvinetso zvekuva neGMM yakawandisa.
Apo chiyero chakawandisa chemapuroteni chinopinda muropa, vanachiremba vane hanya nezvimwe zvinonzi hyperviscosity syndrome, kana HVS. Zviratidzo nezviratidzo zveHVS zvinowanzoita zvinhu zvitatu: kubuda ropa mumucosa, kana kubatana kwezvikamu zvakasiyana-siyana, kuchinja kunoonekwa, uye zviratidzo zvinoratidza kuti chirwere cheshuga chinowanzobva. Kamwe zviratidzo zvemuviri zvinosanganisira kuneta, kuora muviri kana fivha inogonawo kuvapo.
Mishonga inoshandiswa mukurapa lymphoma hainawo kunze kwemigumisiro yavo. Mimwe yemishonga mutsva yemuromo inowanzokonzera chirwere chekudya, nehutachiona huzhinji kana kuti kubatwa.
Muchiitiko chikuru cheKillam, haisi yehutachiona imwe chete inomuchengetedza asi asi pane regimen, uye inotora kubva mumhando dzakasiyana-siyana, kusanganisira mishonga yemagariro, acupuncture, chiropractic therapy, kufungisisa, uye yoga.
"Zvose zvave zvichinyatsobatsira utano hwangu-uye hupenyu hwangu pamwe chete. Oo, uye kuseka-kuseka kunobatsira zvikuru. Saka dzimwe nguva, ndinongotarisa mugirazi uye kuseka! "
> Sources:
> Hunter ZR, Manning RJ, Hanzis C, et al. IgA uye IgG hypogammaglobulinemia muMacroglobulinemia yaWalddenström. Haematologica . 2010; 95 (3): 470-475.
> Gelfand EW.Intravenous immune globulin mune zvirwere zvinoputika uye zvinoputika. N Engl J Med . 2012 Nov; 367 (21): 2015-25.