Chikonzero chekufa kamwe kamwe muvatambi vaduku
Arrhythmogenic right ventricular cardiomyopathy (AVRC) inoshandiswa mumasikirwo ayo maitiro emagetsi anowanzogadziriswa ne fibrous, fatty tissue, zvikurukuru mu ventricle yakarurama. Chikonzero chinoita kuti AVRC inokosha ndechokuti inogona kubudisa mikana inogona kutyisa chirongwa chemwoyo . (AVRC ndiro zita "idzva" rechiitiko ichi, chakashandiswa kunzi "arrhythmogenic right ventricular dysplasia.")
AVRC haina kujairika, asi haisi nyore. Inogona kuwanikwa mune rimwe remakumi maviri evanhu kusvika kune 5000 vanhu vakuru kana iwe uchichitarisa. Zvisinei, nguva bedzi iyo vanhu vakawanda vanowanzozvinzwa pamusoro peVRRC ndeye apo mutambi wechidiki anofa kamwe kamwe, sezvo AVRC imwe yemamiriro emwoyo inobatanidza nekufa kamwe kamwe muvatambi vaduku .
Ndezvipi zviratidzo zveAVRC?
Kunyange zvazvo AVRC iine chirwere chemoyo - ndiko kuti, chirwere chemwoyo - hachiwanzoita zvinokonzera matambudziko emusana anenge akawandisa akakwana kubudisa mwoyo kusakundikana . Pane kudaro, kukosha kwayo kwechirwere chepfungwa ndeyokuti kunogona kukonzera chimiro chechimiro chemaitiro - kunyanya, nguva dzisina kufema dzemagetsi , ventricular tachycardia , uye dzimwe nguva inonzi ventricular fibrillation .
Zviratidzo zvinokonzerwa ne AVRC zvinowanzobatana nearimthmias inogona kubereka. Vanhu vane AVRC vanowanzotsanangurira zvikamu zvekutapira , kuchena, kana kuti syncope . Zvinosuruvarisa, kufa kamwe-kamwe kunogona kuitikawo, uye kunyanya zvinosuruvarisa, kufa kamwe kamwe kunogona kuva chiratidzo chokutanga chekuti pane dambudziko remwoyo.
Kunyange zvazvo AVRC inogona kukonzera kufa kamwe kamwe kunogona kuitika panguva ipi zvayo, chiitiko ichi chinowanzoitika panguva dzezvikamu zvekuita muviri. Ichi ndicho chikonzero AVRC ndechimwe chezviitiko zvinounza rufu rwechimbichimbi mune zvinenge zvakajeka, vatambi vechidiki.
Vanhu vazhinji vane AVRC - kusvika ku40% - havazovi nezviratidzo zvachose, uye vanoongororwa chete kana vakaongororwa nokuda kwechirwere nokuti nhengo yemhuri yakaonekwa kuti ine nayo.
Sei AVRC Inozivikanwa?
Kuongorora ruzivo rweAVRC kunoitwa nokuongorora electrocardiogram (iyo inowanzoratidza kurongeka kwakananga kweQRS yakaoma), uye echocardiogram (iyo inowanzoratidza kuratidzika kusingaenzaniswi mumutsipa wemwoyo we ventricle yakarurama - uye dzimwe nguva kuruboshwe rwemhepo).
Kana chirwere ichi chinoramba chiri mukusahadzika, dzimwe nguva MRI yemwoyo inogona kubatsira kubvisa zvinhu pasi. Kuongorora zvirwere kunogona kubatsirawo pakuita kuti uongororwe, uye zvinokurudzirwa kuvanhu vose vane chirwere ichi.
Kunyangwe electrophysiologic kuedza dzimwe nguva kunobatsira mukusiyanisa tricycardia ye ventricular nekuda kweAVRC kubva kune ventricular tachycardia inokonzerwa nedzimwe mamiriro emwoyo, kuedzwa hakusi nguva dzose kunobatsira, uye hakuwanzodiwi.
Kana chiitiko ichi chikaitwa, kuongorora mazita ekugadzirisa muviri kunorudzirwawo kutanga kwechiremba hama. Inenge imwechete muzvitatu zvekutanga-degree yehukama yemunhu ane AVRC ichapedzisira ichisimudzira chirwere ichi.
Kurapa AVRC
Chinangwa chikuru mukurapa AVRC ndechekudzivirira kufa kamwe kwechirwere chepachiviri kubva kune mhepo inonzi tachycardia kana fibrillation.
Nokuti rufu rwe kamwe kamwe runowanzobatanidzwa nekurovedza mumamiriro ezvinhu aya, vatambi vane AVRC vanofanira kurega pamitambo yose yekukwikwidzana, pamwe chete zvichida kunze kwekudzivirira-kuita zvinhu zvakadai segorofu kana bowling.
Uyezve, vanofanirwa kurega chero basa ripi zvaro rinokonzera kupinza kwakakura.
The arrhythmias inosangana neAVRC inoita seinobudiswa nekunzwira tsitsi-chikamu chehurongwa hwehutongi hwehutongi hunowedzera adrenaline mazinga, uye hunokonzera kurwisana kana kupindura kwechikwata. Ichi ndicho chikonzero chiito chekuita basa chinetso neAVRC. Nokudaro, nyanzvi dzezvemapurisa dzinokurudzira kushandiswa kwe beta blockers mumamiriro ezvinhu aya, kuti tisava nemigumisiro yeadrenaline mumoyo.
Zvinokonzerwa nemagadzirirwo emhepo zvinonyatsorudzirwa kune vanhu vakawanda vane AVRC, kunyanya, kune ani zvake ane chiratidzo chekusungwa kwemwoyo, chikamu chekusimudzira tricycardia, episode ye unexplained syncope, kana kuti echocardiogram inoratidza kubatana kukuru kwemuviri wemwoyo.
Kune vanhu vane AVRC vasina imwe yemamiriro aya, njodzi yekufa kamwe-kamwe inoita seinochera-chero bedzi iyo inotevera mitemo yekuita basa uye inotora mabheji avo.
Mune vanhu vane AVRC avo vakatsigira ventricular arrhythmias, kuonekwa kwenguva refu kunoratidzika kunge kwakanaka chaizvo kana vasingadziviriri maitiro, vanotora beta blockers, kugamuchira zvinogadziriswa, uye (mune dzimwe nguva) kutora antiarrthythmic drug .
Shoko Rinobva
Arrhyhythmogenic right ventricular cardiomyopathy iine maitiro anokwanisa kubudisa zvirwere zvinoparadza mwoyo, uye chimwe chezvikonzero zvinokonzera kufa kamwe kamwe mumitambo yevechidiki. Nechisimba, vanhu vane chirwere ichi vanowanzoita zvakanaka.
> Sources:
> Al-Khatib SM, Stevenson WG, Ackerman MJ, et al. 2017 AHA / ACC / HRS Nhungamiro yekutungamira kwevarwere ne Ventricular Arrhythmias nekudzivirira kwekukurumidza kufa kwechirwere chekufa: Executive Summary: Mharidzo yeAmerican College of Cardiology / American Heart Association Basa reMakirini Emitemo yeChipatimendi Chekuita uye Heart Rhythm Society. Heart Rhythm 2017.
> Ruwald AC, Marcus F, Estes NA 3rd, et al. Association Of Competitive And Recreational Sport Kubatanidzwa Nenzira dzeCardiac Muvarwere NeArrhythmogenic Right Ventricular Cardiomyopathy: Zviwanikwa Kubva North North Multidisciplinary Study Of Arrhythmogenic Right Ventricular Cardiomyopathy. Eur Heart J 2015; 36: 1735.