POEMS syndrome chirwere cheropa chinokanganisa zvikamu zvakawanda zvemuviri uye zvinokonzera zviratidzo zvakawanda. Inobata varume nevakadzi uye kazhinji inotanga mushure mezera remakore makumi mashanu, kunyange zvingaitika kune imwe nguva. Hazvinyatsozivikanwi kuti nguva yakawanda sei POEMS syndrome inowanzoitika nokuti zvakaoma kufungidzira zvakanaka. Chikonzero chacho hachizivikanwi.
Zviratidzo
Izwi rinonzi POEMS rinomiririra:
- P - polyneuropathy, zvinoreva zviratidzo zvehutano zvakadai sekushaya simba, kusungira, uye / kana kushaya simba kwemaoko netsoka
- O - organomegaly, zvinoreva nhengo dzakawedzerwa, kazhinji chiropa, spleen, kana lymph nodes. Inenge 15 muzana yevanhu vane POEMS syndrome vane chirwere chinonzi Castleman (chirwere chinonzi lymph node disorder).
- E - endocrinopathy, zvinoreva kushandiswa pakugadzirwa kwehomoni. Zviratidzo zvakadai sechirwere cheshuga , kusava nesimba , kumisa nguva yekuenda kumwedzi ( amenorrhea ), kuderera kwehutano hwehutachiona (hypothyroidism), uye / kana kunyatsokura muvarume (gynecomastia) inogona kuvapo.
- M - monoclonal gammopathy kana kuti monoclonal plasma yakawandisa chirwere, zvose zvayo zvinoreva kusawanda kweropa mapuroteni masero
- S - ganda rinoshanduka zvakadai sekuwedzera kweganda pigment (hyperpigmentation); kuwedzera bvudzi remuviri (hypertrichosis) pachiso, mitezo, uye pachipfuva; ganda guru nekusimudza, kupfugama (edema) yemakumbo netsoka, kupenya kwezvipikiri.
Vanhu vanogonawo kutarisana, kuneta, maitiro akakura uye marwadzo, kana kuchinja mune zvakaratidzwa, pakati pezvimwe zviratidzo.
Kuziva
Kuongororwa kwePPEMS syndrome kunogona kuitwa zvichienderana nekuongorora kwemuviri uye nhoroondo yezvokurapa. Kuyera ropa kwakafanana nesero yakakwana yeropa (CBC) uye serum protein immunoelectrophoresis yakaitwa kutarisa kusakanganiswa, sezvinoita urini kuongorora. Utachiona hweHyroid, mazinga eropa, uye maestrogen muropa anoedzwa kuti aone kusagadzikana.
Pfupa remapfupa rinoputika uye / kana pfupa x-ray rinogona kuitwa kuti ribatsire pakuonekwa.
Munhu anonzi ane PEMEMS syndrome kana "P" (polyneuropathy) uye "M" (zvisingawanzo ropa reprotein) zviripo pamwe chete ne sclerotic (scarring) zvipembenene zvepfupa kana Castleman chirwere. Vanhu vazhinji vachave nezvimwe zviratidzo zvechirwere zvakare. Nemhaka yokuti vanachiremba vakawanda havazive nePPEMS syndrome, zvirwere zvisingaenzaniswi zvekutsvaga ropa zvinowanzokonzera kusarudzwa kwemashoko akawanda eeseloma, kana zviratidzo zve polyneuropathy zvinokonzera kusagadziriswa kwechirwere chisingagumi chinokonzera kuderedza polyneuropathy (CIDP).
Kurapa
Kurapa kwePEMEMS syndrome kunobva mukurapa kwechikonzero chepachivi chetachiona cheropa. Vazhinji vanhu vanowana mishonga yekurapa yakadai sokuti:
- Radiation therapy
- Corticosteroid mishonga yakadai sa prednisone
- Chemotherapy
- Hormone kushandiswa kwemahomoni ari pasi
- Physical therapy
- Tora marora kudururira
Nyanzvi dzakadai sedyeredzi (chirwere chinotyisa chirwere), hematologist (chirwere cheropa chirwere), dermatologist (chiremba weganda), uye endocrinologist (hormone gland doctor) inowanzobatanidzwa mukutarisira munhu ane POEMS syndrome.
Sources:
Dispenzieri, Angela. "POEMS Syndrome." Hematology 2005 (2005): 360-367.
Dispenzieri, Angela, Robert A. Kyle, Martha Q. Lacy, S. Vincent Rajkumar, Terry M. Therneau, Dirk R. Larson, Philip R. Greipp, Thomas E. Witzig, Rita Basu, Guillermo A. Suarez, Rafael Fonseca, John A. Lust, & Morie A. Gertz. "POEMS syndrome: tsanangudzo uye kwenguva refu." Ropa 101 (2003): 2496-2506.
"Zviratidzo zvePPOEMS Syndrome." Kurapa kwePEMEMS Syndrome paMayo Clinic. The Mayo Clinic. 22 May 2007
Chan, Joanna, & Wingfield Rehmus. "POEMS Syndrome." eMedicine. 15 Dec 2006. WebMD. 22 May 2007