Myopathy izwi rinoshandiswa kurondedzera zvirwere zvemuviri. Kana iwe wakamboonekwa uine myopathy, kana kuti iwe uri kuongororwa nokuda kwekugona kukanganisa, pane mukana wakasimba wekuti iwe hauna kunzwa pamusoro pekuita myopathy kusvikira ikozvino, nokuti haisi kufanana nezvimwewo zvirwere zvehutano. Iwe unogona kuva nemibvunzo pamusoro pekugadzirisa chirongwa, chii chaunofanira kutarisira maererano nemashoko ekufananidzira uye kurapwa, uye kana dzimwe nhengo dzemhuri yako dzingave dziri pangozi yekunyunyuta.
Chii Chinonzi Myopathy?
Myopathy inoreva chirwere chemisungo. Apo munhu ane chirwere chemisungo, misumbu inoshanda zvishoma kudarika pane yainofanira. Izvozvo zvinogona kuitika kana masimba asingatauri zvakanaka, kana atovadzwa, kana kuti paanoshayiwa zvikamu zvinokosha.
Misumbu inowanzoshanda nekontracting, zvinoreva kuva shoma. Mushonga unojairika unoumbwa nemapurotini uye zvimwe zvivako zvakagadzirwa nenzira yakarongeka kuti zvibvumirane nemisumbu. Kana chimwe chezvikamu izvi zvikakosha, izvi zvinogona kukonzera myopathy.
Kune zvikonzero zvakasiyana-siyana zvakasiyana-siyana zvehutachiona hwehutachiona, uye nekuda kweizvozvo, kune mhando dzakasiyana dzakasiyana-siyana. Chimwe chee myopathie yakasiyana ine zita rayo chaiyo, chinokonzera, chinangwa chekuongororwa, kuongororwa, nekurapa. Zvimwe myopathies zvinotarisirwa kuipa kupfuura nguva, asi dzimwe dzisina kusimba. Myopathie yakawanda inhaka, uye mazhinji haasi.
Zviratidzo
Muzhinji, myopathy inokonzera musimba utera. Nzira yakanyanya kufanana yekushaya simba inorondedzerwa sechinhu chakanyanya kusimba. Izvi zvinoreva kuti mishonga yemaoko ekumusoro nemakumbo epamusoro zvinonyanya kuoma kudarika zvisikwa zvemaoko kana tsoka. Dzimwe nguva, myopathy inokanganisa mafungiro ekufema (mishonga inodzora kufema).
Mamwe maitiro ekunyunyisa kunosanganisira kuneta, kusava nesimba, uye kuwedzera kukundikana sezvo zuva richienderera mberi kana kuti kusimba kusimba nekuedza.
Kakawanda, apo vanhu vave nemafungiro kwemakore, musimba inrophy inotanga kukura, iyo iri kuonda uye kuparara kwemisungo, kuderedza simba remisungo kunyanya. Myopathy inowanzobatanidzwa nechimiro chisina kujairika chemapfupa, kazhinji nokuti hutachiona husingaregi hudzivirira mapfupa kuti asachengetedze maitiro avo.
Ndingaziva Sei Kana Ndine Myopathy?
Kazhinji, myopathy inonetsa kuongororwa. Kana iwe uine zviratidzo zvemyopathy, pane mukana wakasimba wekuti iwe uchatora kuendesa kune unyanzvi hwehutano kana rheumatologist, kana zvose zviri zviviri, zvichienderana nechimwe chezviratidzo zvako chinonyanya kuzivikanwa.
Kuongorora kuongororwa kunosanganisira kuongororwa kwepanyama, kusanganisira kuongorora kweganda rako, mafungiro ako, simba rako remasumbu, rako reyeri uye manzwiro ako. Chiremba wako achatora nhoroondo yezvokurapa uye anokubvunza nezvemhuri yako yezvokurapa.
Panewo mimwe miedzo yaunogona, zvichienderana nehutano hwehutano hwako uye zviwanikwa zvekuongorora kwako muviri. Iyi miedzo inosanganisira kuongororwa kweropa, sekuenzanisa kweropa rakazara (CBC) uye mazinga e electrolyte.
Mimwe miedzo yeropa inosanganisira erythrocyte sedimentation rate (ESR) uye antinuclear antibody test (ANA), iyo inofanana nokuputika. Zvisikwa kinase muropa zvinogona kuongorora kuparara kwemisimba. Zvirwere zvehurosi, miviri yemagetsi uye endocrine inogona kudiwa.
Chimwe chiedzo chinonzi electromyography (EMG) inomutambo wegetsi unotarisa misi inoshanda kuburikidza nekushandiswa kweesingano dzinoona humwe hutano hwehutachiona hwehutano hwako nekufamba. Dzimwe nguva, miedzo yakakosha yakadai semisumbu yehuputi uye kuongorora mazita evanhu anogona kubatsira kuongorora dzimwe mhando dzemyopathy.
Aina
Congenital myopathy zvinoreva kushamwaridzana kunoitwa nomunhu.
Zvizhinji zvezviitiko izvi zvinotendwa kuva nhaka kana kudarika kuburikidza nemhuri nemagetsi. Uye, apo zviratidzo zve congenital myopathies zvinowanzotanga pachidiki, izvo hazvisi nguva dzose. Dzimwe nguva chirwere chepachirwere chinotarirwa hachina kutanga kuratidza zviratidzo kusvikira munhu achiri kuyaruka kana kunyange munhu mukuru.
Kazhinji mararamiro anowanikwa nhaka anosanganisira :
- Mitochondrial myopathy : Ichi ndicho chirwere chinokonzerwa nechirema mune chikamu chekubudisa magetsi chese, chinonzi mitochondria . Kune marudzi mazhinji emitochondrial myopathy, uye apo iyo inogona kukonzerwa nekuchinja kwemararamiro (kusagadzikana mumagenene) inogonawo kuitika pasina chero nhoroondo yemhuri zvachose.
- Mabopathy yeMetabolic : Ichi iboka rezvirwere zvinokonzerwa nezvinetso zvemagetsi zvinopesana nebasa remuviri. Kune mazita akasiyana-siyana akasiyana-siyana anokonzerwa nemasikisi emyopathies anokonzerwa nezviremera mumakemikari anonyora kune mamwe maitiro ezvakakosha kumusana musimba.
- Nemaline myopathy : Ichi chikamu chekushungurudzika chinoratidzwa nekuvapo kwezvivako zvinonzi 'nemaline rods' mumasumbu. Nemaline myopathy inowanzobatanidzwa ne kupemha musimba utera.
Congenital myopathies dzinosanganisira:
- Central Central Myopathy : Ichi ndicho chiitiko chinokonzerwa nehupenyu chinokonzera kusava nesimba, matambudziko emapfupa, uye kukanganisa kwakanyanya kune mamwe mishonga. Kuoma kwechirwere ichi kunopesana, zvichikonzera kushaya simba kwakanyanya pakati pevamwe vanhu uye kushaya simba kwakanyanya kune vamwe.
- Muscular dystrophy : Ichi iboka rezvirwere zvinokonzerwa nokusakara kwemisungo kana masero emasumbu asingazivikanwe. Nenzira, muscular dystrophy haisi myopathy, asi inowanzowirirana mune zviratidzo, saka iwe unogona kutanga kuwana chirongwa chekurapa chinotarisirwa kuziva kana iwe une myopathy kana muscular dystrophy. Mhedzisiro huru pakati pekushaya myopathy uye muscular dystrophy ndeyekuti mishonga haigoni kushanda zvakanaka mu myopathy, asi mishonga inopera mu muscular dystrophy.
Myopathy inogonawo kukonzerwa nehutano hwakasiyana-siyana hunobatanidza zvinetso zvepanyama pane kuwedzera kune nenyaya nemisungo inopesana.
Myopathies inowanikwa kazhinji inosanganisira:
- Inflammatory / autoimmune myopathy : Izvi zvinoitika apo muviri unozvirwisa, zvichikonzera kuora kwemisungo kana kupindira musimba basa. Kune boka reMyopathies rinoratidzirwa nekuputika mukati kana pedyo nemisungo. Mimwe yemamiriro aya anosanganisira polymyositis , dermatomyositis, sarcoidosis, lupus, uye rheumatoid arthritis.
- Myopathy inotyisa : Izvi zvinoitika kana chepfu, mishonga, kana kuti zvinodhaka zvinokanganisa musimba maitiro kana basa.
- Endocrine myopathy : Izvi zvinoitika apo chirwere chemahomoni chinovhiringidza musimba basa. Zvinonyanya kukosha zvinosanganisira utachiona kana zvinetso zvegrenal gland.
- Utachiona hwehutachiona : Izvi zvinogona kuitika kana utachiona hunoita kuti mishonga ishande zvakanaka.
- Myopathy iri pasi pekusawirirana kwe electrolyte : Zvinetso zveElectrolyte, zvakadai sepamusoro-soro kana pasi pedasium, zvinogona kukanganisa basa remisungo.
Chii Chandinofanira Kutarisira Kana Ndiine Myopathy kana Myopathy Inogona Kuitika?
Muzhinji, congenital myopathy inotarisirwa kuwedzera kuwedzera kana kugadzikana munguva yakawanda uye haisi kutarisirwa kuvandudza. Myopathies dzisina kufanana, zvakadai sekupindira, kushandiswa kwemagetsi, kana kuti myopathie inotyisa, inogona kuvandudza kana chikonzero chemyopathy chiri kunyatsochengetedzwa.
Kuwana hukama hwakanaka hwehutano hwako hwakakosha kuve nechokwadi kuti une chimiro chakanaka chinogoneka. Kana uine rudzi rwemyopathy huri kutarisirwa kuvandudza, iwe unofanirwa kunyatsoteerera nyaya dzakadai seatrophy, zvinodzvinyirira, uye kuve nechokwadi chokuti iwe unoramba uchibatanidzwa mukurapa kwemuviri kuitira kuti ugone kushanda zvakanaka.
Kurapa
Iko hakusi kurapwa kunobatsira kunogona kuchinja zvakare kana kuporesa mishonga yako kuti upore myopathy. Kana pane chikonzero chinozivikanwa, chakadai sechinetso chekuguma, kugadzirisa chinokonzera chinogona kubatsira kuvandudza zviratidzo zvemyopathy, kana kuti zvingabatsira kudzivirira kuti irege kukura.
Kakawanda, kubatsirwa nekuputika ndiyo chinhu chinonyanya kukosha mune myopathy, kuitira kuti kufema kwako kunogona kuchengetedzwa zvakanaka.
Mhuri Yangu Ichawana Myopathy Kana Ndine Myopathy Here?
Hongu, mamwe myopathies zvechokwadi ane nhaka. Kana iwe uine runyararo rwekuzvarwa, ipapo pane mukana wekuti vamwe vehama dzako, vana vako, vakomana, uye vazukuru, kana dzimwe hama dzaigonawo kukudziridza myopathy. Zvakakosha kuita kuti mhuri yako izive nezvehutano hwako, sezvo chirwere chekare chinogona kuvabatsira kuti vawane kurapwa kwekare uye kutarisirwa.
Zvimwe zvemyopathies dzisingatauri zvakananga kuberekwa kana kuti nhaka dzinogona kunge dziine tsika yekufambisa mumhuri, saka mhuri yako inogona kuwedzera mungozi kunyange kana iwe une myopathy isingazivikanwi kuti inhaka.
Shoko Rinobva
Myopathy haisi yakajairika. Chirwere chemusana chinogona kuparadza mararamiro ako ehupenyu. Zvisinei, vanhu vazhinji vanoonekwa kuti vane myopathy vanogona kuchengetedza hupenyu hunogutsa, kusanganisira kuchengetedza basa rinogutsa uye kufara nemhuri inofadza uye yehupenyu hwevanhu.
> Sources:
> Lundberg IE, Miller FW, Tjärnlund A, Bottai M, J, Kuziva uye kuenzaniswa kweidiopathic inflammatory myopathies, Intern Med. 2016 Jul; 280 (1): 39-51