Nzvo dzenyu dziri nhengo mbiri dzakagadzirwa nenyuchi dziri pasi pembambo yenyu. Basa ravo guru nderokuisa ropa kuitira kuti ribvise muviri wemarara uye huwandu hwemvura.
Immunoglobulin Netafropathy (IgA nephropathy) chinetso chepfungwa chinokanganisa glomerulus, iyo inonzwisisika mitero yeropa inobata basa rekutsvaga ropa.
Overview
Chimwe chetsvo dzako chinosvika mamiriyoni ephrononi, uye nephron imwe neimwe ine glomerulus.
Aya marumeriki kana masero mashoma emidziyo yeropa anonyanya kuisa ropa rako. Vanotumira zvinhu zvakasvibiswa uye zvinoshandiswa (semuviri) kumukaka uye kusunungura ropa nemamwe maserolekiti makuru, sepuroteni, kudzokera muropa remvura.
Kazhinji, zvirwere zvemuviri zvevanhu zvinosunungura an anti-antibody, immunoglobulin A, mukupindura kune chimwe chinhu chinokonzerwa nehutachiona hwehutachiona. Asi kune vanhu vane IgA nephropathy, immunoglobulin A inovaka uye inozviisa mukati me glomeruli yeinso dzavo.
Iyi immunoglobulin A buildup inokonzera kuora kwepvo, uye pakupedzisira kupera, izvo zvinoita kuti zvive nyore kuti glomeruli iite basa rayo rokutsvaga. Somugumisiro, kusvuta kwetsvo kunogona kuitika.
Statistics
MuNorth America, inenge kaviri kupfuura yevarume kupfuura vakadzi vane IgA nephropathy, uye izvi zvine chokuita nevana nevakuru. Mukuwedzera pakuva yakajairika mune zvevarume, IgA nephropathy inonyanya kuwanikwa muCaucasians neAsia uye inowanikwa muAfrica-America.
Pakupedzisira, muUnited States, inopfuura hafu yevanhu vakuru, makore makumi matatu kana kupfuura kana panguva yekufungidzirwa kweGIA nephropathy, itai danho 3 kusvika kune imwe nhanho 5 chirwere chisingaperi chepfungwa. Izvi zvinoratidzira kuti kuongorora IgA nephropathy yapfuura kungave kunobatsira, sezvo kurapwa kunogona kukanganisa kushanda kwemunhu kwepfungwa kunonoka.
Kuziva
Izvo zviratidzo zviviri zvakajairika zveIgA nephropathy iropa mumuguta , iyo inokonzera urini kutarisa tema-mavara, uye mapuroteni mumuguta , izvo zvinogona kuita kuti murini uonekwe sewuru.
Zvisinei, ruzhinji rwevanhu vane IgA nephropathy havana zviratidzo. Kana munhu akacherechedza ropa rakawandisa mumuviri wavo, uye vane IgA nephropathy, inowanzotora hutachiona hwehutachiona hwehutano kana chirwere chemudumbu.
Nezvo, chiremba angangokufungidzira iwe kana munhu waunoda ane IgA nephropathy inobva munhoroondo yakanyatsocherechedza, uyewo uchapupu huri muhuta uye kuongorora ropa. Kuti asimbise kuongororwa, ane nephrologist (chiremba anonyanya kugadzirisa zvirwere zvepfungwa) achabvisa chiduku chiduku chetsvo. Iyi nzira inonzi biopsy uye inogadzirwa nekuisa saga mumusana wako, uko inokwanisa kuwanikwa nyore nyore.
Mushure mokunyora, chirwere chepachichechecha chichaongorora mishonga yepso pasi pema microscope uye ichiipisa kuti ione kana kwete IgA mari iripo. Kana pane uchapupu hweGigA buildup, izvi zvichasimbisa kuongororwa kwegA nephropathy.
Zvakakosha kucherechedza kuti vanachiremba havakwanisi kuita tsvina yepso pamusoro pemunhu wese ane ropa shoma kana mapuroteni mumuguta wavo.
Pane kudaro, kana uine ropa kana mapuroteni mumuguta wako, chiremba wako anogona kutarisa urinhi yako uye basa repvo mwedzi mitanhatu kusvika kumi nembiri kana zvakadaro.
Anogona kuita bhiopsy kana maitiro ako epimpinotanga kuchera (sezvinopupurirwa nekwakakwirira ye creatinine pamubvunzo weropa) kana iwe unotanga kuwedzera kuwanda kwemapuroteni kurasikirwa mumuguta wako.
Kuva nehuwandu hwehutachiona hunogonawo kuva chikonzero nei chiremba wako achiita ainso biopsy (kana panewo ropa uye / kana mapuroteni mumuguta).
Kurapa
Muvanhu vanoona kuti vane IgA nephropathy, kusvika kusvika hafu inononoka zvishoma (makore anopfuura makumi emakore) inova nekuguma kwepfungwa yekusuwa kwepfungwa (inonzi end-stage renal disease, kana ESRD).
Zvichienderana nezvimwe zvinhu zvinoenderana neAgA yako nephropathy, chiremba wako anogona kukubata nemishonga yekudzikisa kupfuurira kwezvirwere zvepfungwa dzako.
Iyi mishonga inosanganisira angiotensin-kuchinja enzyme (ACE) inhibitors kana angiotensin II receptor blockers (ARBs) kuti utonge ropa rako. Mafuta ehove zvokudya zvinowedzera zvinowanzokurudzirwa.
Chiremba wako anogonawo kubata kutura kunoitika ne IgA nephropathy nekukupa steroid seforenisone.
Kana iwe uchifambira mberi kusvika pakuguma kwetachiona chirwere chepfungwa, unogona kurapwa ne dialysis kana kupora kwepvo .
Nepo kuchinjwa kwetsvo kusarudzo, haisi kuonekwa sechirapa, sezvinonzi neAgA nephropathy inogonazve kugadzikana mumutsvo ichangobva kuiswa.
Shoko Rinobva
Zvingave iwe iwe kana munhu waunoda akawanikwa ane IgA nephropathy, imwe chirwere chetsvo, kana akawanikwa ane ropa uye / kana mapuroteni mumuguta wako, iva nechokwadi chekutevera pamwe nachiremba wako sezvawakarayirwa.
Izvi zvinoramba zvakanyatsoitika neIgA nephropathy, sezvo zvakaoma chaizvo kuvanachiremba kuti vataure kuti ndiani achava akanaka uye ndiani achakurira chirwere chepfungwa yekupedzisira.
> Sources:
> Cheung CK, Barratt J. (2017). Clinical presentation uye kuongororwa kwegA nephropathy. Glassock RJ, Fervenza FC, ed. UpToDate, Waltham, MA: UpToDate Inc.
> National Institute of Diabetes and Digestive and Kidney Diseases (2014). Zvitsvo Zvako uye Maitiro Azvo Anoshanda.
> IgA Nephropathy Foundation yeAmerica. (nd). FAQs - Chii chinonzi IgA Nephropathy?
> Wyatt RJ, Julian BA. IgA nephropathy. N Engl J Med. 2013 Jun 20; 368 (25): 2402-14.