Mycosis fungoides (MF) ndiyo inowanzosangana neT-cell lymphomas , boka revanhu vasingawanisi kanzera rinokura muganda. Sezary syndrome, iyo inonyanya kuumbwa, inowanikwa munenge ma5% ematambudziko ose e mycosis fungoides. MuUnited States, anenge 1000 mitsva itsva ye mycosis fungoides inoitika gore rose.
MF inobata varume kaviri kakawanda sevakadzi, uye inowanzoonekwa kuvanhu vemavara kupfuura vanhu vachena.
Mycosis fungoides inogona kutanga chero ipi zvayo, asi iyo yakanyanya kufanana nemakore makumi mashanu. Chikonzero chechirwere hachizivikanwi.
Zviratidzo zveMycosis Fungoides
Mycosis fungoides inokura mumatanho, ayo anotsanangurwa nezviratidzo zveganda, kusanganisira:
- Chikamu chechikamu - Ganda rinokura, rakatsvuka; mune vanhu vane ruvara rwemavara, izvi zvinogona kuonekwa sechinhu chakajeka kana chema. Izvi zvivara zveganda zvakanyanyisa. Dzimwe nzvimbo dzinogona kusimudzwa uye dzakaoma, uye dzinozivikanwa seplate. Mavara nemarata zvinowanzoonekwa pamabako, kugomera, mahudyu, pasi pezvanza, uye pamazamu / chifuva.
- Nhengo dzeganda zvikamu - Red-violet yakasimudza mashizha (majeeti) anooneka uye angave akafanana nemafuta (akaita mushwa) kana kuti ave nechirwere.
- Girazi tsvuku (erythroderma) gadziro - Mukuwedzera kumakumbo nemakumbo, ganda romumwe munhu rinogona kukura nzvimbo dzakakura dzvuku dzakatonyanya uye dzakanyanya. Ganda recheche muchiso rinogona kuvhara, uye ganda rezvimiti nemichindwe rinogona kuvhara uye kuputika.
- Lymph node nzvimbo - Mukati ino, mycosis fungoides inotanga kutamira kune dzimwe nhengo dzomuviri. Nzvimbo dzekutanga dzakakanganiswa ndezvenymini nodes, iyo inogona kupiswa, uye kazhinji inova nekenza. MF Kanza inogonawo kupararira kuchiropa, mapapu, kana marora.
Kuongororwa kweChiitiko
Uyu mamiriro anozivikanwawo seAlibert-Bazin syndrome kana granuloma fungoides.
Kazhinji, pane makore anenge matanhatu kubva panguva iyo zviratidzo zvinotanga kusvika kuongororwa kwemycosis fungoides. Nechirwere ichi, kuvhiringidzika nemamwe mamiriro ezvinhu kwakajairika sezvo zvikamu zvepakutanga zvechirwere zvinowanzofananidzira eczema kana psoriasis.
Kuti uwane hutano hwemycosis fungoides, muenzaniso weganda unogona kutorwa ( chivara cheganda ) uye kuongororwa nokuda kwechirwere chacho. Kuongororwa kwebhizinesi kunogona kuitwa kuti uone kufambira mberi kwekenza.
Kuti anzwisise zvikamu zvakasiyana zvechirwere, kuongorora kwakasiyana-siyana kunoitwa kuongorora lymph nodes, ropa uye nhengo dzomukati. Vakawanda vanorwara vanoratidza zviratidzo zvinongovharirwa paganda, zvakadai semaruva (nzvimbo dzakapoteredza) uye plaques (zvishoma kana kuti 'wrinkled' nzvimbo).
Kurapa kweMF
Kana mycosis fungoides iri muchitanga chekutanga, mishonga yakadai steroid creams, chirwere chechiedza, chemotherapy inoshandiswa paganda, kana kuti masikironi emisipiresi inogona kushandiswa. Chinangwa ndechekuisa kenza yemuMF mukuregererwa, izvo zvinogona kugara kwenguva yakareba.
Kana chirwere cheumwe munhu chisingapindi kune marapirwo emaperembudzi, kana chirwere chacho chafambira mberi kusvika kumarara, zvirongwa zvakadai se recombinant alfa interferon kana chemotherapy inogona kushandiswa. Zvinosuruvarisa, hapana mushonga we mycosis fungoides, saka nguva yakawanda munhu anorarama nayo nechirwere ichi chinoenderana nekureba kwacho kwakapararira nenguva iyo inowanikwa uye chirwere chinotanga.
Kunobva:
Pinter-Brown, LC (2002). Mycosis fungoides. eMedicine.